A: If you notice a very distinct sweet smell as you urinate, this could mean one of two things: maple syrup urine disease or diabetic ketoacidosis (DKA). … Sweat and urine smells like maple syrup; milk and/or breastfed baby may smell like maple syrup. Cat Urine Gets Worse With Time. I read something about Maple Sypup Urine Disease but he says that his urine does not smell like that. 1. share. That smell could be due to one of the following reasons: 1. We use cookies to give you the best possible experience on our website. Do you mysteriously smell maple syrup everywhere? I drink 1 large mug of coffee every day. Is Lupituss syrup safe to take for dry cough? my cat smells like maple syrup. Cat urine that’s outside the litter box is usually unnoticed until it becomes a problem. Why does my dog’s urine smell like maple syrup? Genetic and Rare Diseases Information Center (GARD) - PO Box 8126, Gaithersburg, MD 20898-8126 - Toll-free: 1-888-205-2311 Premium Questions. Then, Rachel unexplainably goes into a coma, but fortunately, doctors are able to diagnose her with maple syrup urine disease (MSUD). Sweet-smelling urine can also indicate diabetes mellitus, because excess blood sugar finds its way into the urine. Maple Syrup Urine Disease. Additional Reading: 7 Steps to Take … Causes. This leads to a buildup of these chemicals in the blood. The infant is usually lethargic, feeds poorly, vomits and has a developmental delay. Species:Cat. Unless you know for sure that they only smell because of an isolated potty accident, having the underlying issue diagnosed is the best move. Luna, She doesn't like wet food - Answered by a verified Cat Veterinarian. If you have problems viewing PDF files, download the latest version of Adobe Reader. The symptoms of other forms of MSUD start in adolescence or adulthood. I switched to coffee because I have severe withdrawal if I don't get any caffeine. What could be causing this? People with this disorder aren't meant to eat protein, meaning this is the one, single good reason to go vegan. There's a disease in humans called maple syrup urine disease caused by a defect in a metabolic enzyme required to break down branched chain amino acids... Could possibly occur in a cat? Urine Smells Like Eggs: Causes. I don’t know why something would smell like maple syrup in a house that is constructed like it is. The urine smell could be the result of what you are eating. Maple syrupe urine disease (MSUD) is an autosomal recessive metabolic disorder that leads to the accumulation of branched-chain amino acids. He told me that it has for a very long time and he never knew why. So many foods can be responsible for making your urine smell like eggs. Maple syrup urine disease (MSUD) is a rare, inherited metabolic disorder. It still smells like maple syrup. It is inherited in an autosomal recessive pattern. My dog is a shiba, and they're the cats of the dog world, so maybe that's it! The bedroom, the closet and … dog smells like fritos. What is maple syrup urine odor Honey vs sugar vs maple syrup Connect by text or video with a U.S. board-certified doctor now — wait time is less than 1 minute! If you notice your dog’s urine is smells like maple syrup, it could be a sign of canine diabetes. Suggest treatment for maple syrup urine disease . The earwax and urine of infants with MSUD smells like maple syrup. Asparagus is a good example. Diagnosis of MSUD is based on the symptoms, clinical exam, and blood and urine testing. The result is your pee smells like maple syrup as the chemical buildup from undigested leucine, isoleucine, and valine changes how your urine smells. It's usually discovered at an early age because of the fact the the baby's urine smells like maple syrup. shes totally healthy. Pills like Oxycontin or Percocet give off a sweet smell as they burn. Urine, sweat, or earwax that smells like maple syrup or burnt sugar. An inherited condition, maple syrup urine disease, so named because it causes urine to smell like sweet maple syrup, results from the body's inability to digest certain amino acids. 8. Does diabetes run in you family? Since Rachel Webb was born, she has had urine that smells like maple syrup, cries constantly for no reason, has feeding problems, and has bouts of unresponsiveness. Info please on maple sugar urine disease~what foods to avoid ~have 14 mo old who tested neg for PKU @ birth and today has maple smelling urine. I'd think a maple syrup smelling pig is much more desirable than a stinky smelling pig! Excessive levels of sugar in the urine can also cause it to smell of maple syrup, though this is often described as a more sickly-sweet smell. Maple syrup urine disease is a metabolic disorder that causes certain amino acids to build up in … Maple syrup urine disease or ketoacidemia is an inherited disorder, where the body lacks certain enzymes that break down amino acids. I am 17 -- 5' 10'' -- 128lbs. Sweet-Smelling Urine Medically reviewed by Alana Biggers, M.D., MPH Find out why your urine smells sweet or fruity, what’s causing this symptom, and treatment methods. MSUD is caused by genetic variants in the BCKDHA, BCKDHB, or DBT genes. The type of Freon is R410A some say it a leak. Changes in muscle tone – poor muscle tone, muscle tightness/tension So I Googled it and only find a few people posting the honest question, maybe one or two honest answers and then the thread of absurdities. This may not always be present in all types. Sweet-smelling urine can also indicate diabetes mellitus, because excess blood sugar finds its way into the urine. Why? For language access assistance, contact the NCATS Public Information Officer. A rare genetic condition, maple syrup urine disease causes problems with breaking down some amino acids in the proteins you consume. This condition causes the urine of an infant to have a distinct, sweet, maple syrup-like odor. (This disorder got its name from this common symptom.) It is caused by a defect in 1 of 3 genes. 2. share. My cat's pee smells like syrup, but I just took him to the vet and got his blood and urine tested and he's healthy. Charlie: Yeah. MD. Once discovered, the baby is given a protein free diet that it … level 1. C. Lybol, DEM (midwife) 1 mom found this helpful Users frequently say the smoke tastes and smells like sugar and burnt marshmallows. Maple syrup urine disease (MSUD) is inherited, which means it is passed down through families. Not just like something sweet. It's not both underarms every time either, might be just one or the other that day. lol. Charlie: Well, it’s the bedroom-Tom: Those smell questions are tough. My pee smells like maple syrup!!! It … I think my cat has been lying or rolling in some aromatic plants or weeds nearby. Other signs and symptoms of this disease is urine or sweat that smells of maple syrup, diffuculty concentrating, lethargy, vomiting, seizures and death. It is usually picked up on the metabolic screen the state does on newborns. Seriously-pancake syrup. If you do have this disease it is very serious and you need to be seen by a doctor immediately. Report Save. Urine smells like cough syrup . The last few years I have been drinking Coke every day -- 1-3 cans/day. Diet. MD. You probably don’t have maple syrup urine disease because it’s a rare inherited disorder that affects an estimated 1 in 185,000 infants worldwide, according to the National Institutes of Health. Among worldwide Maple syrup urine disease (MSUD) affects about 1 out of 185,000 babies. The disease prevents your body from breaking down certain amino acids. MSUD is more common in certain ethnic groups but also it is seen in many countries. I have let this machine run for hours . My kidneys started to hurt slightly from time to time, so I quit drinking. I just noticed that my boyfriends sweat smells like maple syrup. Cat urine is not all that different from other animals’ urine, but what gives cat urine such a bad smell? Opiates are typically the only kind of pills that are smoked. Strange smells. We started looking for the GI problems in November-so it wasn't long after that. My cat smells like maple syrup too. Original Poster 1 year ago. level 2. An inherited condition, maple syrup urine disease, so named because it causes urine to smell like sweet maple syrup, results from the … So many things can make your urine smell like eggs or sulfur. Maple syrup urine disease. Poor feeding, vomiting, loss of appetite, irritability. Occasionally causes loose stools, which go away when fenugreek is discontinued. Use of more than 100 grams of fenugreek seeds daily can cause intestinal distress and nausea (recommended dose is less than 8 grams per day). The urine of people with this condition can smell like maple syrup. Fritos seem to be the universal dog smell. Early treatment is vital. An inherited condition, maple syrup urine disease, so named because it causes urine to smell like sweet maple syrup, results from the body's inability to digest certain amino acids. There is metabolic condition which causes urine to smell like maple syrup. Want to know more about maple syrup urine disease and its symptoms? Maple syrup urine disease (MSUD) is inherited, which means it is passed down through families. My spayed 1 year old cat has started smelling like maple syrup. Research studies show that about 1 out of every 380 babies from the Old Order Mennonite population is affected by this condition. Please go in right away. Maple syrup urine disease (MSUD) is a disorder in which the body cannot break down certain parts of proteins. There is a disease called Maple Syrup Urine Disease, no joke...but infants are tested for it and I don't know if you can even develop it later in life. In humans there is a disease called maple syrup urine disease where one of the signs is a sweet syrup smell to urine. Then I go days without smelling it. About 2 months ago, I swore my urine {a little darker than usual that day} smelled like it. Q: Why does my urine smell like maple syrup? There can also be cases where your dog actually smells like maple syrup or their urine is foamy, both signs of possible trouble that shouldn’t be ignored. Sluggish/slow/tiredness and weakness. But, your baby may have been missed. Report Save. Absolutely, but as far as that goes, I’d investigate the walls. People with this condition cannot break down the amino acids leucine, isoleucine, and valine. 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